While PSC is a relatively rare cholangiopathy that presents more commonly in the Caucasion male population, LT is the only therapy that can reverse or correct resulting end-stage liver disease.

Review the clinical characteristics, liver biochemistry, and the range of complications that can present in biliary atresia; as well as the recommended treatments and follow-up.

Cystic fibrosis affects nearly 1 in every 3000 live births, and is the most common fatal autosomal recessive disease among Caucasians. There's a wide spectrum of liver disease among CF patients, from steatosis, to cirrhosis, and severe portal hypertension.

HCC is rare in early childhood but is the second most common pediatric liver malignancy and often presents in school age children and adolescents.

Cardiac complications are crucial factors in morbidity and mortality while on the organ waiting list, making careful diagnosis, workup, and tailored treatment is essential for managing cardiopulmonary complications in end-stage liver disease in children.

Audible Article by Michael P. Manns and Richard Taubert

Audible Article by Meredith Borman and Mark G. Swain

Cardiac complications are crucial factors in morbidity and mortality while on the organ waiting list, making careful diagnosis, workup, and tailored treatment is essential for managing cardiopulmonary complications in end-stage liver disease in children.

HCC is rare in early childhood but is the second most common pediatric liver malignancy and often presents in school age children and adolescents.

Cystic fibrosis affects nearly 1 in every 3000 live births, and is the most common fatal autosomal recessive disease among Caucasians. There's a wide spectrum of liver disease among CF patients, from steatosis, to cirrhosis, and severe portal hypertension.