Host: Shira Johnson, MD
Guest: Gregory P. Cosgrove, MD, FCCP
Guest: Sonye K. Danoff, MD, PhD
Guest: Christina Garcia, MD, PhD
Guest: Victor J. Thannickal, MD
Idiopathic pulmonary fibrosis (IPF) is the most common and lethal of the idiopathic interstitial pneumonias, accounting for as many as 40,000 deaths per year in the United States. There is no cure for IPF, and although two recently approved drugs have been shown to delay progression, prognosis remains poor, with an estimated median survival of about 4 years. Recent research into the genetics and the pathophysiology of the disease has identified a number of potential therapeutic targets that offer hope for improving the management – and potentially for preventing – the disease. The availability of a nationwide Clinical Care Network focused on IPF and the launch of a patient registry are other developments that have improved the outlook for patients and their caregivers. Clinicians would benefit from hearing summaries of scientific presentations by leading experts in IPF from the recent Pulmonary Fibrosis Foundation's PFF Summit.